Anne W' Lucky, M'D'

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Interdisciplinary Care ofEpidermolysis Bullosa

• Anne W. Lucky, M.D.
• Professor of Dermatology and Pediatrics
• The Cincinnati Childrens EB Center
• The Cincinnati Childrens Hospital
• Cincinnati, Ohio
• USA

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Traditional Care
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Multidisciplinary Care
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Interdisciplinary Care
Integrated Care Plan
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Interdisciplinary EB Care

• Dermatology and Nursing
• Wound care
• Protective bandaging, clothing, shoes
• Infection control
• Patient education and support
• Nutrition and GI
• Adequate caloric intake
• Esophageal strictures and webs
• Deficiencies of Fe, Zn, et al.
• Osteopenia / osteoporosis
• Constipation

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Interdisciplinary EB Care

• Hematology
• Anemia of chronic illness
• Iron deficiency
• Oncology
• Squamous cell carcinoma
• Cardiology
• Cardiomyopathy
• Selenium and carnitine deficiencies

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Interdisciplinary EB Care

• Surgery (General, Plastic, Hand)
• Esophageal dilatation
• Feeding gastrostomy
• Excision and grafting of SCC
• Hand Releases
• Dentistry
• Prophylactic hygiene
• Decay, crowding, oral blistering
• Anesthesiology
• Anesthesia
• Pain Control

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Interdisciplinary EB Care

• Occupational and Physical Therapy
• Hand function / splints
• Aids to daily living
• Whirlpool under anesthesia
• Ophthalmology
• Corneal Abrasions
• Radiology
• Ba swallow
• Intraoperative fluoroscopy
• Pathology
• Diagnosis of EB
• SCC

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Interdisciplinary EB Care

• Gynecology
• Induction of puberty
• Contraception
• Pregnancy
• Psychology
• Family dynamics
• Behavior modification
• Adolescent adjustment
• Pain and depression
• Drug and alcohol addiction
• Social Services
• Financial issues
• School adjustment
• Career counseling
• Family Support

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Interdisciplinary EB Care

• Future Therapies
• Biologically active dressings and grafts
• Protein replacement or supplementation
• Gene therapy
• In vitro
• In vivo

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Cincinnati Childrens EB Center Team

• Anne W. Lucky,MD
• Richard G. Azizkhan, MD
• Michael K. Farrell, MD
• Jean Whalen,RN
• Kim Hazelbaker,RN
• Susan Rowe,RN
• Marie Callen, DMD
• Kristina Steinau, PT
• Mary Flaspohler, OT
• Jennifer Phillips, RD,CSP,LD
• Linda Wallace. LISW
• Kenneth R. Goldschneider,MD
• Peter Stern, MD
• Denise Adams, MD
• Eric P. Wittkugel, MD
• Edgar T. Ballard, MD
• Anne Lynch, PhD
• John Racadio, MD
• Jill Huppert, MD

• Co Director, Pediatric Dermatology
• Co-Director, Pediatric Surgery
• Pediatric Gastroenterology
• Clinical Care Coordinator
• Clinical Care Coordinator
• Clinical Care Coordinator
• Dentistry
• Physical Therapy
• Occupational Therapy
• Nutrition
• Social Services
• Pain Management
• Hand Surgery
• Oncology
• Anesthesiology
• Pathology
• Psychology
• Radiology
• Gynecology

www.cincinnatichildrens.org/eb-center