Accumulation

1
HYPERPROLINEMIA TYPE II In Homo sapiens
  Nitric-oxide synthase P29475

  Nitric-oxide synthase P29475

Argininosuccinic acidHMDB00052

N-(omega)-HydroxyarginineHMDB04224

Citrate cycle
Nitric oxideHMDB03378

Fumaric acidHMDB00134

Alanine Aspartate metabolism
CitrullineHMDB00904
L-Aspartic acidHMDB00191

L-ArginineHMDB00517

Arginine-tRNA ligase Q5T160
CarbamoylphosphateHMDB01096

Glycine amidinotransferase P50440
Ornithine carbamoyltransferase A8K9P2
Accumulation
D-Arginineand D-Ornithine metabolism
OrnithineHMDB00214
Carbamoyl-phosphate synthase P31327
UreaHMDB00294
Amino acid metabolism
D-Arginineand D-Ornithine metabolism
Guanidoacetic acid
HMDB00128
L-Glutamic acidHMDB00148
d
Guanidinoacetate N-methyltransferase Q14353

Creatine HMDB00064

L-d-1-Pyrroline-5-carboxylic
acidHMDB01301
Proline dehydrogenase, mitochondrial O43272
Pyrroline-5- carboxylate reductase
A8K798
Accumulation
Bifunctional amino
acyl-tRNA synthetase P07814
Accumulation
D-ProlineHMDB03411

Peptide
Image Not Available from HMDB
Accumulation
 Proline dehydrogenase A6NF53

Pyrroline-5-carboxylate reductase A8K798
Peroxisome
1-Pyrroline-4-hydroxy-2-carboxylate HMDB02
234 d
4-Hydroxy-L-glutamate HMDB02273
d
Proline dehydrogenase, mitochondrial
A6NF53
4-Hydroxy-2-oxoglutaric acid HMDB02070
d