Case of the week: Number 0602. High Risk HCM

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Case of the week Number 06-02. High Risk HCM
Case from Carolyn McCarthy, Perry Elliott, The
Heart Hospital, London, England History An 33
year old man with HCM with a family history of
sudden death. Seven years previously, a single
Holter had shown 3 beats of NSVT. Cine CMR shows
HCM with ASH, no SAM, no LVOTO (left or right),
and normal systolic function. After gadolinium,
there was very extensive late enhancement, (44
of LV myocardium, arrowed). The scan triggered
re-evaluation of cardiac risk, and the patient
was offered an ICD. Conclusion Extensive late
enhancement indicating scar in HCM, particularly
at a young age, is associated with clinical risk
markers. (reference here) Members only How I
image HCM (Sanjay Prasad) here