osteopetrosis

1
osteopetrosis

• ?. ???? ?????? ????
• 20/09/2005

2
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• -????? ??????? .
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  ?????? .
  
  

3
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4

• ???????? - ????? ?????? 11q13
• -????? ?????? 1p21
• - ??????? ?????? ????????
  ?????? ???? ???
• ?? ????? ?????????? ???????

5

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6
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8
?????? ??????

• ???? ?? ??????? ???????
• ????????? ???????? ??? ?? ???? , ????? ????? ?
  ??????, ?????? ??? , ???? ?? ??????? , ???? ????
  ??????? ?? ??? ????? ?????? , ???? ????? .

9
?????? ??????

• ???? ?????? ??????????(40 ?? ?????? ?? ??????) .
• ????????? ???????? ??? ?? ???? , ???? ????? ,
  ?????? ????? ????? ???? , ??? ????? ?????? ??
  ???? ?????? .

10
?? ????? ????? ?????? ??????
???????? Type I Type II
???? ??????? ???? ?? ????? ??????? ?????? ???? ?? ??????? ??????? ??????
?????? ?????? ?? ???? ?????? ?????? ???? ???? rugger jersey
????? ?? ???? ???? ?????? ???? ???? ?????? ?? ?????
???? ??? ?? ?? metaphyse ????? ?? ???? ?? ??
??? ???? ??? ????? ?????
?????????? ??????? ?????? ?????? ????
11
????????? ????????

• ????? ??????? ???????? ????? ??? ???? ????? ????
  ??? ????? ? ????? .
• ?????? ????? ??????? ??????? .
• ?????? ???????? .
• ????? ??metaphyse .
• ????? rugger jersey , ???? ?????????? .
• ??????? ????? ?????? ?????? ??????? .
• ??? ????? ???? ??????? ??????? ??????? ?????
  ????? .

12
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13
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14
????????? ????????

• ??????? ????????? ????????? ??? PTH ?????? .
• ??????? ?????????? ??????? ?? ???? ?????? ?????
  ???? ??????? ?????????? ??????? ?????? .
• ?????? ?? ????????? ????? ????? .

15
??????? ????????

• Pyknodysostosis
• Camurati - Engelmann disease
• Pyle disease
• Metal poisoning
• ?????????? ???????
• ??? ???? ????? ?????
• ??? ?????
• ??? ???? ???????

16
??????? ? ??????????

• ?????? ??????? ???? ?? ????? ?????? .
• Coxa vara
• ??? ????? ?????? ?????? ?? ???? ?????? .

17
??????

• ?????? ?????? - ??? ??? ?????
• - ??? ???? ?? ????? ?????
  
• - ????? Prednisolone ,
  Calcitonine , Calcitriol ,Interferon .
  
• ?????? ?????? ??? ????? ????? ???? .

18
???????? ???? ?? ????? ??????? ???????

• ???? ?????? ????? ???? ????? .
• ???? ???? ??? ???????? ????? ?? ??????? ???????
  ????? .
• ???? ???? ???? ??? ???? ?????? ?????? ?? ?? Coxa
  vara .
• ?????? ??????? ??????? ? ??????? .
• ??????? ??????? ????? ??????? ?????? ??????? ?
  ??? ???????? .

19
MoKazem.com

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  ??????? ?? ??? ??????? ???????? ?? ???? ???????
  ??????? ?? ???? ????, ??? ????? ?. ???? ??????.
• ?????? ??? ????? ?? ??????? ??????? ?? ???
  ????????.
• This lecture is one of a series of lectures were
  prepared and presented by residents in the
  department of orthopedics in Damascus hospital,
  under the supervision of Dr. Bashar Mirali.
• This site is not responsible of any mistake may
  exist in this lecture.

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Dr. Muayad Kadhim